The diagnostic signature of Susac’s syndrome

  • Todd A. Hardy
    Address: Neuroimmunology Clinic, Concord Repatriation General Hospital, University of Sydney, Australia.
    Neuroimmunology Clinic, Concord Repatriation General Hospital, University of Sydney, Australia

    Brain & Mind Centre, University of Sydney, NSW, Australia
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      • Susac’s syndrome is frequently misdiagnosed.
      • Callosal snowballs are best seen on sagittal FLAIR MRI brain sequences.
      • Fundus fluorescein angiography (FFA) is vital for diagnosis.
      • Early diagnosis and treatment may limit end-organ damage.


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