Abstract
Sporadic inclusion body myositis (sIBM) is a slowly progressive idiopathic inflammatory
myopathy. The characteristic early quadriceps and finger flexor muscle weakness often
leads to the diagnosis of sIBM, especially when all canonical pathological features
of sIBM are not present on muscle biopsy. Weakness of the paraspinal muscles, resulting
in head drop and/or camptocormia, is a rare clinical finding along the course of sIBM,
and even more rare as the presenting feature. We describe two patients with sIBM manifesting
with camptocormia as the sole clinical manifestation for several years prior to the
diagnosis by muscle biopsy. This observation emphasizes the role of sIBM in the etiology
of camptocormia and the need to consider this common myopathy as a cause of weakness,
despite the lack of classic quadriceps and finger flexor muscle weakness years after
the onset of the paraspinal muscle weakness.
Keywords
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Article info
Publication history
Accepted:
June 10,
2013
Received:
June 4,
2013
Identification
Copyright
© 2013 Elsevier Ltd. Published by Elsevier Inc. All rights reserved.
