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Case Report| Volume 16, ISSUE 12, P1665-1667, December 2009

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Septo-optic dysplasia with encephalocele

  • Alagappan Periakaruppan
    Affiliations
    Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Medical College Junction, Trivandrum 695011, Kerala, India
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  • Hima S. Pendharkar
    Correspondence
    Corresponding author. Tel.: +91 989 5649529; fax: +91 471 2446433.
    Affiliations
    Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Medical College Junction, Trivandrum 695011, Kerala, India
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  • Arun Kumar Gupta
    Affiliations
    Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Medical College Junction, Trivandrum 695011, Kerala, India
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  • Bejoy Thomas
    Affiliations
    Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Medical College Junction, Trivandrum 695011, Kerala, India
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  • C. Kesavdas
    Affiliations
    Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Medical College Junction, Trivandrum 695011, Kerala, India
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      Abstract

      Septo-optic dysplasia is a rare congenital anomaly presenting with visual deficits or pituitary dysfunction. We report the first case of septo-optic dysplasia associated with encephalocele, partial callosal agenesis, polymicrogyria and subcortical nodular heterotopia.

      Keywords

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