Advertisement
Case report| Volume 12, ISSUE 4, P472-474, May 2005

Download started.

Ok

Empty sella, hypogonadism and hypopituitarism secondary to moyamoya disease

      Summary

      We report the case of a young male who presented at the age of 34 years with intracranial hemorrhage due to moyamoya disease. He was later diagnosed with hypogonadism and hypopituitarism. Chromosomal evaluation revealed a normal karyotype. The results of further neuroradiological studies led to the diagnosis of empty sella syndrome.

      Keywords

      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'

      Subscribe:

      Subscribe to Journal of Clinical Neuroscience
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect

      References

        • Suzuki J.
        • Takaku A.
        Cerebrovascular ‘moyamoya’ disease. Disease showing abnormal net-like vessels in base of brain.
        Arch Neurol. 1969; 20: 288-299
        • Ikeda H.
        • Sasaki T.
        • Yoshimoto T.
        • et al.
        Mapping of familial moyamoya disease gene to chromosome 3p24.2-p.26.
        Am J Hum Genet. 1999; 64: 533-537
        • Inoue T.K.
        • Ikezaki K.
        • Sasazuki T.
        • et al.
        Linkage analysis of moyamoya disease on chromosome 6.
        J Child Neurol. 2000; 15: 179-182
        • Gosalakkal J.A.
        Moyamoya disease:a review.
        Neurol India. 2002; 50: 6-10
        • Stanfield J.P.
        The blood supply of the human pituitary gland.
        J Anat. 1960; 94: 257-273
        • Ahmadi J.
        • Keane R.J.
        • George S.
        • McCormick G.S.
        • Fallis R.J.
        • Miller C.A.
        Ischemic chiasmal syndrome and hypopituitarism associated with progressive cerebrovascular occlusive disease.
        AJNR Am J Neuroradiol. 1984; 5: 367-372
        • Kaye A.H.
        • Tress B.M.
        • Brownbill D.
        Intracranial pressure in patients with empty sella syndrome without benign intracranial hypertension.
        J Neurol Neurosurg Psychiatry. 1982; 45: 209-216
        • Kaufman B.
        The “empty” sella turcica - a manifestation of the intrasellar subarachnoid space.
        Radiology. 1968; 90: 931-941
        • MacKenzie C.A.
        • Milner R.D.G.
        • Bergvall U.
        • Powell T.
        Growth failure secondary to moyamoya syndrome.
        Arch Dis Child. 1990; 65: 232-233
        • Mootha S.L.
        • Riley W.J.
        • Brosnan P.G.
        Hypothalamic pituitary dysfunction associated with moyamoya disease in children.
        J Pediatr Endocrinol Metab. 1999; 12: 449-453
        • Komiyama M.
        • Yashui T.
        • Sakatomo H.
        • et al.
        Basal meningoencephalocele, anomaly of optic disc and panhypopituitarism in association with moyamoya disease.
        Pediatr Neurosurg. 2000; 33: 100-104
        • Maira G.
        • Anile C.
        • De Marinis L.
        Cerebrospinal fluid pressure and prolactin in empty sella syndrome.
        Can J Neurol Sci. 1990; 17: 92-94